{"id":2492,"date":"2025-11-10T10:59:22","date_gmt":"2025-11-10T09:59:22","guid":{"rendered":"https:\/\/cfnorge.no\/?page_id=2492"},"modified":"2026-01-08T15:46:34","modified_gmt":"2026-01-08T14:46:34","slug":"behandling","status":"publish","type":"page","link":"https:\/\/cfnorge.no\/en\/pcd\/behandling\/","title":{"rendered":"Treatment"},"content":{"rendered":"<p>[et_pb_section fb_built=&raquo;1&#8243; next_background_color=&raquo;#ffffff&raquo; _builder_version=&raquo;4.21.0&#8243; _module_preset=&raquo;default&raquo; background_color=&raquo;gcid-9e2f3af2-1007-4221-b250-8e35d98c5991&#8243; background_enable_image=&raquo;off&raquo; background_size=&raquo;custom&raquo; background_image_width=&raquo;101%&raquo; bottom_divider_style=&raquo;wave&raquo; global_colors_info=&raquo;{%22gcid-9e2f3af2-1007-4221-b250-8e35d98c5991%22:%91%22background_color%22%93}&raquo;][et_pb_row _builder_version=&raquo;4.21.0&#8243; _module_preset=&raquo;default&raquo; max_width=&raquo;900px&raquo; custom_margin=&raquo;|auto|77px|auto||&raquo; global_colors_info=&raquo;{}&raquo;][et_pb_column type=&raquo;4_4&#8243; _builder_version=&raquo;4.21.0&#8243; _module_preset=&raquo;default&raquo; global_colors_info=&raquo;{}&raquo;][et_pb_text _builder_version=&raquo;4.21.0&#8243; _module_preset=&raquo;default&raquo; header_font=&raquo;Poppins|600|||||||&raquo; header_text_color=&raquo;gcid-26e97d0d-b127-4ce1-b597-0df3fb01df24&#8243; custom_margin=&raquo;||1px|||&raquo; hover_enabled=&raquo;0&#8243; global_colors_info=&raquo;{%22gcid-26e97d0d-b127-4ce1-b597-0df3fb01df24%22:%91%22header_text_color%22%93}&raquo; sticky_enabled=&raquo;0&#8243;]<\/p>\n<h1><span data-contrast=\"none\" xml:lang=\"NB-NO\" lang=\"NB-NO\" class=\"TextRun SCXW45429628 BCX0\"><span class=\"NormalTextRun SCXW45429628 BCX0\">Treatment<\/span><\/span><span class=\"EOP SCXW45429628 BCX0\" data-ccp-props=\"{&quot;335559738&quot;:300,&quot;335559739&quot;:150}\">\u00a0<\/span><\/h1>\n<p>[\/et_pb_text][et_pb_text _builder_version=&raquo;4.21.0&#8243; _module_preset=&raquo;default&raquo; text_font=&raquo;Poppins|300|||||||&raquo; text_text_color=&raquo;gcid-26e97d0d-b127-4ce1-b597-0df3fb01df24&#8243; text_font_size=&raquo;16px&raquo; text_line_height=&raquo;1.8em&raquo; hover_enabled=&raquo;0&#8243; locked=&raquo;off&raquo; global_colors_info=&raquo;{%22gcid-26e97d0d-b127-4ce1-b597-0df3fb01df24%22:%91%22text_text_color%22%93}&raquo; sticky_enabled=&raquo;0&#8243;]<\/p>\n<p>Det finnes ingen \u00e5rsakskorrigerende behandling for PCD enn\u00e5, men anbefalt behandling og oppf\u00f8lging kan ved noen tilfeller gi et tiln\u00e6rmet normalt liv. M\u00e5let er \u00e5 hjelpe kroppen med \u00e5 bli kvitt slim og \u00e5 forebygge infeksjoner som kan gi komplikasjoner som lungeskader og nedsatt lungefunksjon.<\/p>\n<p>Slimmobiliserende lungebehandling med inhalasjoner er en viktig del av den daglige forebyggende behandlingen. Inhalasjon av saltvann p\u00e5 forst\u00f8verapparat inng\u00e5r i lungebehandlingen for \u00e5 gj\u00f8re slimet l\u00f8sere og lettere \u00e5 fjerne. Fysisk aktivitet er viktig og kan inng\u00e5 i behandlingen for \u00e5 l\u00f8sne og fjerne slimet. Personer med PCD f\u00e5r ogs\u00e5 god oppl\u00e6ring i ulike puste- og hosteteknikker for \u00e5 kunne fjerne slimet. Neseskylling kan ogs\u00e5 v\u00e6re effektivt for \u00e5 l\u00f8sne slim i nese og bihuler, og anbefales derfor for alle med PCD. De yngste barna kan bruke saltvanns-spray eller dr\u00e5per. St\u00f8rre barn, ungdom, og voksne kan ha god effekt av neseskylling med nesehorn eller spr\u00f8yter.<\/p>\n<p>I de kommende \u00e5rene er \u00f8kt forskningsaktivitet er forventet, og det er viktig for utvikling av behandling og prognose ved PCD. M\u00e5lsettingen er best mulig lungehelse og livskvalitet for personer som lever med PCD i fremtiden.<\/p>\n<p>[\/et_pb_text][\/et_pb_column][\/et_pb_row][\/et_pb_section][et_pb_section fb_built=&raquo;1&#8243; _builder_version=&raquo;4.21.0&#8243; _module_preset=&raquo;default&raquo; custom_padding=&raquo;26px|||||&raquo; global_colors_info=&raquo;{}&raquo;][et_pb_row _builder_version=&raquo;4.21.0&#8243; _module_preset=&raquo;default&raquo; max_width=&raquo;900px&raquo; custom_margin=&raquo;|auto|22px|auto||&raquo; global_colors_info=&raquo;{}&raquo;][et_pb_column type=&raquo;4_4&#8243; _builder_version=&raquo;4.21.0&#8243; _module_preset=&raquo;default&raquo; global_colors_info=&raquo;{}&raquo;][et_pb_image src=&raquo;https:\/\/cfnorge.no\/wp-content\/uploads\/2024\/07\/voksenliv-med-CF-artikkel-header.jpg&raquo; title_text=&raquo;voksenliv-med-CF-artikkel-header&raquo; _builder_version=&raquo;4.21.0&#8243; _module_preset=&raquo;default&raquo; custom_margin=&raquo;||41px|||&raquo; hover_enabled=&raquo;0&#8243; global_colors_info=&raquo;{}&raquo; sticky_enabled=&raquo;0&#8243;][\/et_pb_image][\/et_pb_column][\/et_pb_row][et_pb_row _builder_version=&raquo;4.21.0&#8243; _module_preset=&raquo;default&raquo; max_width=&raquo;900px&raquo; global_colors_info=&raquo;{}&raquo;][et_pb_column type=&raquo;4_4&#8243; _builder_version=&raquo;4.21.0&#8243; _module_preset=&raquo;default&raquo; global_colors_info=&raquo;{}&raquo;][et_pb_text _builder_version=&raquo;4.21.0&#8243; _module_preset=&raquo;default&raquo; header_font=&raquo;Poppins|600|||||||&raquo; header_text_color=&raquo;gcid-26e97d0d-b127-4ce1-b597-0df3fb01df24&#8243; custom_margin=&raquo;||1px|||&raquo; hover_enabled=&raquo;0&#8243; global_colors_info=&raquo;{%22gcid-26e97d0d-b127-4ce1-b597-0df3fb01df24%22:%91%22header_text_color%22%93}&raquo; sticky_enabled=&raquo;0&#8243;]<\/p>\n<h1><span data-contrast=\"none\" xml:lang=\"NB-NO\" lang=\"NB-NO\" class=\"TextRun SCXW45429628 BCX0\"><span class=\"NormalTextRun SCXW45429628 BCX0\">Smittevern og hygiene<\/span><\/span><span class=\"EOP SCXW45429628 BCX0\" data-ccp-props=\"{&quot;335559738&quot;:300,&quot;335559739&quot;:150}\">\u00a0<\/span><\/h1>\n<p>[\/et_pb_text][et_pb_text _builder_version=&raquo;4.21.0&#8243; _module_preset=&raquo;default&raquo; text_font=&raquo;Poppins|300|||||||&raquo; text_text_color=&raquo;gcid-26e97d0d-b127-4ce1-b597-0df3fb01df24&#8243; text_font_size=&raquo;16px&raquo; text_line_height=&raquo;1.8em&raquo; hover_enabled=&raquo;0&#8243; locked=&raquo;off&raquo; global_colors_info=&raquo;{%22gcid-26e97d0d-b127-4ce1-b597-0df3fb01df24%22:%91%22text_text_color%22%93}&raquo; sticky_enabled=&raquo;0&#8243;]<\/p>\n<p>Personer med PCD har et svekket immunforsvar og kan derfor ikke bekjempe sykdomsfremkallende mikrober som ellers hos allmennbefolkningen. Forebyggende smitteverntiltak er derfor helt avgj\u00f8rende for \u00e5 beskytte helsen og bevare lungefunksjonen best mulig gjennom livet. Internasjonalt samarbeider eksperter kontinuerlig om \u00e5 vurdere og oppdatere anbefalinger for smittevern, blant annet for \u00e5 hindre smitte mellom personer med PCD eller lignende sykdommer, og for \u00e5 unng\u00e5 egen-smitte via urent utstyr.<\/p>\n<p>Grunnlaget for godt smittevern er gode hygienerutiner: grundig h\u00e5ndvask, hostehygiene og regelmessig desinfisering av utstyr og overflater. Ved daglig lungebehandling skal man alltid bruke rent inhalasjonsutstyr for slimmobilisering. Det frar\u00e5des ogs\u00e5 \u00e5 ha n\u00e6rkontakt med andre som har PCD eller lignende sykdommer hvis dere ikke bor sammen. Dette betyr likevel ikke at man m\u00e5 unng\u00e5 sosiale sammenkomster med andre med diagnosen. Det er fullt mulig \u00e5 m\u00f8tes p\u00e5 en trygg m\u00e5te. For eksempel arrangerer NFCF jevnlig treff og samlinger, som den \u00e5rlige l\u00e6ringshelgen, der deltakerne kan treffes trygt ved \u00e5 f\u00f8lge gjeldende smittevernregler for NFCF.<\/p>\n<h3><a name=\"_Toc218772901\"><\/a><\/h3>\n<p>[\/et_pb_text][et_pb_toggle title=&raquo;Oppf\u00f8lging&raquo; open=&raquo;on&raquo; open_toggle_text_color=&raquo;gcid-edcc47c2-e936-4ba2-8e6c-8ca8cb2c2a05&#8243; open_toggle_background_color=&raquo;gcid-9e2f3af2-1007-4221-b250-8e35d98c5991&#8243; closed_toggle_background_color=&raquo;gcid-9e2f3af2-1007-4221-b250-8e35d98c5991&#8243; icon_color=&raquo;gcid-edcc47c2-e936-4ba2-8e6c-8ca8cb2c2a05&#8243; toggle_icon=&raquo;&#x22;||divi||400&#8243; use_icon_font_size=&raquo;on&raquo; icon_font_size=&raquo;18px&raquo; open_icon_color=&raquo;gcid-edcc47c2-e936-4ba2-8e6c-8ca8cb2c2a05&#8243; open_toggle_icon=&raquo;&#x21;||divi||400&#8243; _builder_version=&raquo;4.21.0&#8243; _module_preset=&raquo;default&raquo; title_text_color=&raquo;gcid-edcc47c2-e936-4ba2-8e6c-8ca8cb2c2a05&#8243; title_font=&raquo;|600|||||||&raquo; body_text_color=&raquo;gcid-26e97d0d-b127-4ce1-b597-0df3fb01df24&#8243; body_link_text_color=&raquo;gcid-edcc47c2-e936-4ba2-8e6c-8ca8cb2c2a05&#8243; custom_margin=&raquo;||62px|||&raquo; custom_padding=&raquo;35px||35px||false|false&raquo; border_width_all=&raquo;0px&raquo; box_shadow_style=&raquo;preset3&#8243; locked=&raquo;off&raquo; global_colors_info=&raquo;{%22gcid-edcc47c2-e936-4ba2-8e6c-8ca8cb2c2a05%22:%91%22icon_color%22,%22open_toggle_text_color%22,%22title_text_color%22,%22body_link_text_color%22,%22open_icon_color%22%93,%22gcid-26e97d0d-b127-4ce1-b597-0df3fb01df24%22:%91%22body_text_color%22%93,%22gcid-9e2f3af2-1007-4221-b250-8e35d98c5991%22:%91%22open_toggle_background_color%22,%22closed_toggle_background_color%22%93}&raquo;]<\/p>\n<p>I Norge f\u00f8lges pasienter med PCD ved Nasjonalt sjeldensenter \u2013 lungesykdommer og cystisk fibrose, OUS i Oslo og ved Haukeland universitetssykehus. Personer med PCD har behov for tverrfaglig oppf\u00f8lging av fagpersoner med kompetanse p\u00e5 PCD. Alle b\u00f8r f\u00e5 oppf\u00f8lging av barnelege\/lungelege, fysioterapeut, spesialsykepleier, \u00f8re-nese-hals-spesialist, eventuelt psykolog, klinisk sosionom og klinisk ern\u00e6ringsfysiolog. Med god behandling og oppf\u00f8lging vil omkring to tredjedeler ha en ganske stabil lungefunksjon.<\/p>\n<p>&nbsp;<\/p>\n<p>[\/et_pb_toggle][et_pb_toggle title=&raquo;Antibiotika&raquo; open_toggle_text_color=&raquo;gcid-26e97d0d-b127-4ce1-b597-0df3fb01df24&#8243; open_toggle_background_color=&raquo;RGBA(255,255,255,0)&raquo; closed_toggle_background_color=&raquo;gcid-edcc47c2-e936-4ba2-8e6c-8ca8cb2c2a05&#8243; icon_color=&raquo;gcid-def3f79a-900d-4425-86b8-efdc1c9633a6&#8243; toggle_icon=&raquo;&#x50;||divi||400&#8243; use_icon_font_size=&raquo;on&raquo; icon_font_size=&raquo;20px&raquo; open_icon_color=&raquo;gcid-edcc47c2-e936-4ba2-8e6c-8ca8cb2c2a05&#8243; open_toggle_icon=&raquo;&#x4f;||divi||400&#8243; open_use_icon_font_size=&raquo;on&raquo; open_icon_font_size=&raquo;20px&raquo; _builder_version=&raquo;4.21.0&#8243; _module_preset=&raquo;default&raquo; title_text_color=&raquo;#FFFFFF&raquo; title_font=&raquo;|600|||||||&raquo; title_font_size=&raquo;18px&raquo; body_text_color=&raquo;gcid-26e97d0d-b127-4ce1-b597-0df3fb01df24&#8243; body_link_text_color=&raquo;gcid-edcc47c2-e936-4ba2-8e6c-8ca8cb2c2a05&#8243; custom_margin=&raquo;10px||10px||false|false&raquo; custom_padding=&raquo;||||false|false&raquo; hover_enabled=&raquo;0&#8243; border_width_all=&raquo;0px&raquo; locked=&raquo;off&raquo; global_colors_info=&raquo;{%22gcid-def3f79a-900d-4425-86b8-efdc1c9633a6%22:%91%22icon_color%22%93,%22gcid-26e97d0d-b127-4ce1-b597-0df3fb01df24%22:%91%22open_toggle_text_color%22,%22body_text_color%22%93,%22gcid-edcc47c2-e936-4ba2-8e6c-8ca8cb2c2a05%22:%91%22open_icon_color%22,%22closed_toggle_background_color%22,%22body_link_text_color%22%93}&raquo; sticky_enabled=&raquo;0&#8243;]<\/p>\n<p>I perioder med \u00f8kt slimdannelse og infeksjoner i lunger og luftveier kan individer med PCD ha behov for antibiotikabehandling. Dette kan gis som mikstur eller tabletter\/kapsler, som inhalasjon eller som en infusjon med plastkateter inn i blod\u00e5ren (intraven\u00f8st).<span data-ccp-props=\"{&quot;335559739&quot;:150}\"><\/span><\/p>\n<p>[\/et_pb_toggle][et_pb_toggle title=&raquo;Vaksinasjon&raquo; open_toggle_text_color=&raquo;gcid-26e97d0d-b127-4ce1-b597-0df3fb01df24&#8243; open_toggle_background_color=&raquo;RGBA(255,255,255,0)&raquo; closed_toggle_background_color=&raquo;gcid-edcc47c2-e936-4ba2-8e6c-8ca8cb2c2a05&#8243; icon_color=&raquo;gcid-def3f79a-900d-4425-86b8-efdc1c9633a6&#8243; toggle_icon=&raquo;&#x50;||divi||400&#8243; use_icon_font_size=&raquo;on&raquo; icon_font_size=&raquo;20px&raquo; open_icon_color=&raquo;gcid-edcc47c2-e936-4ba2-8e6c-8ca8cb2c2a05&#8243; open_toggle_icon=&raquo;&#x4f;||divi||400&#8243; open_use_icon_font_size=&raquo;on&raquo; open_icon_font_size=&raquo;20px&raquo; _builder_version=&raquo;4.21.0&#8243; _module_preset=&raquo;default&raquo; title_text_color=&raquo;#FFFFFF&raquo; title_font=&raquo;|600|||||||&raquo; title_font_size=&raquo;18px&raquo; body_text_color=&raquo;gcid-26e97d0d-b127-4ce1-b597-0df3fb01df24&#8243; body_link_text_color=&raquo;gcid-edcc47c2-e936-4ba2-8e6c-8ca8cb2c2a05&#8243; custom_margin=&raquo;10px||10px||false|false&raquo; custom_padding=&raquo;||||false|false&raquo; hover_enabled=&raquo;0&#8243; border_width_all=&raquo;0px&raquo; locked=&raquo;off&raquo; global_colors_info=&raquo;{%22gcid-def3f79a-900d-4425-86b8-efdc1c9633a6%22:%91%22icon_color%22%93,%22gcid-26e97d0d-b127-4ce1-b597-0df3fb01df24%22:%91%22open_toggle_text_color%22,%22body_text_color%22%93,%22gcid-edcc47c2-e936-4ba2-8e6c-8ca8cb2c2a05%22:%91%22open_icon_color%22,%22closed_toggle_background_color%22,%22body_link_text_color%22%93}&raquo; sticky_enabled=&raquo;0&#8243;]<\/p>\n<p>I tillegg til \u00e5 f\u00f8lge det nasjonale programmet for barnevaksinasjoner er det anbefalt \u00e5rlig vaksinasjon mot influensa for barn som er over 6 m\u00e5neder gamle. Videre b\u00f8r barn under ett \u00e5r f\u00e5 tilf\u00f8rsel av immunglobuliner mot RS-virus. \u00a0For voksne med PCD anbefales det \u00e5 f\u00f8lge det nasjonale programmet for vaksinering hos voksne (oppfriskningsvaksiner og nye vaksiner). <a href=\"https:\/\/www.fhi.no\/\">Folkehelseinstituttets<\/a> anbefalinger for sesongvaksinering som \u00e5rlig influensavaksine og andre aktuelle vaksiner for personer med lungesykdommer gjelder ogs\u00e5 ved PCD.<\/p>\n<p>[\/et_pb_toggle][\/et_pb_column][\/et_pb_row][\/et_pb_section][et_pb_section fb_built=&raquo;1&#8243; disabled_on=&raquo;on|on|off&raquo; _builder_version=&raquo;4.21.0&#8243; _module_preset=&raquo;default&raquo; background_color=&raquo;gcid-f60bfea8-f451-489d-8bfd-27e12ee36365&#8243; custom_padding=&raquo;||0px||false|false&raquo; global_colors_info=&raquo;{%22gcid-f60bfea8-f451-489d-8bfd-27e12ee36365%22:%91%22background_color%22%93}&raquo;][et_pb_row column_structure=&raquo;1_2,1_2&#8243; _builder_version=&raquo;4.21.0&#8243; 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